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[P096] A case of linear atrophoderma of Moulin
( Ji Hyun Kim ) , ( Sook Hyun Kong ) , ( Seok Hyun Han ) , ( Yong Woo Oh ) , ( Yu Sung Choi ) , ( Tae Heung Kim ) , ( Ho Seok Suh )
프로그램북 69권 1호 344-345(2pages)
UCI I410-ECN-0102-2018-500-000373922
이 자료는 4페이지 이하의 자료입니다.

Linear atrophoderma of Moulin (LAM) is a rare acquired disorder most commonly arising during childhood or adolescence. Pathogenesis is unclear but it is thought to be caused by mosaicism caused by a postzygotic mutation. It is characterized by asymptomatic hyperpigmented atrophic band-like lesions localized mostly on the trunk following the lines of Blaschko. Distribution is usually unilateral, and extensive lesions with bilateral involvement are extremely rare. Histopathologic findings of LAM reveal hyperpigmentation of the epidermis, thickened dermal collagen fibers and a focal reduction of subcutaneous fatty tissue. No effective treatment options have been discovered for LAM but prognosis is favorable with no systemic involvement. A 12-year-old girl presented with 5-month history of multiple linear atrophic hyperpigmented plaques along the lines of Blaschko on the face, neck and extremities. Histopathologic findings from the plaque showed a normal epidermis with a hyperpigmented basal layer and loss of subcutaneous fat. The patient was diagnosed with LAM and treated with a combination of topical steroid and narrow band UVB phototherapy twice weekly. Herein we report a case of linear atrophoderma of Moulin.

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